Cardiac MRI of Arrhythmogenic Right Ventricular Dysplasia
Description: Authors: Sun Moon Kim, MD; Steve Leung, MD, FACC. A 56-year-old male with repolarization abnormalities on electrocardiogram (ECG), ventricular arrhythmias, and family history of sudden cardiac death presents with worsening shortness of breath and undergoes cardiac magnetic resonance imaging (MRI). Four-chamber, steady-state free precession cine imaging demonstrates areas of aneurysms at the right ventricular apex with akinesis of the free wall. The right ventricle is severely dilated (right ventricular end-diastolic volume index [RVEDVi ]of 215 mL/m2) with severely depressed ejection fraction (15%), which meets cardiac MRI major criteria for arrhythmogenic right ventricular dysplasia.
Date: June 18, 2015
Clinical Topics: Arrhythmias and Clinical EP, Heart Failure and Cardiomyopathies, Noninvasive Imaging, Vascular Medicine, Implantable Devices, Genetic Arrhythmic Conditions, SCD/Ventricular Arrhythmias, Atrial Fibrillation/Supraventricular Arrhythmias, Acute Heart Failure, Magnetic Resonance Imaging
Keywords: Aneurysm, Arrhythmias, Cardiac, Arrhythmogenic Right Ventricular Dysplasia, Cardiomyopathies, Death, Sudden, Cardiac, Dyspnea, Electrocardiography, Heart Ventricles, Magnetic Resonance Imaging, Magnetic Resonance Spectroscopy, Stroke Volume, Heart Failure